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Question 19#

Which of the following is not characteristic of prunebelly syndrome?

A. Bilateral intra-abdominal testes
B. Dilatation of the ureters
C. Dilatation of the urinary bladder
D. Malformed renal parenchyma

Correct Answer is D

Comment:

Prune-belly syndrome refers to a disorder that is characterized by extremely lax lower abdominal musculature, dilated urinary tract including the bladder, and bilateral undescended testes. The term prune-belly syndrome appropriately describes the wrinkled appearance of the anterior abdominal wall that characterizes these patients. The incidence is significantly higher in men, and patients manifest a variety of comorbidities, the most significant of which is pulmonary hypoplasia, which is not survivable in the most severe cases. Skeletal abnormalities include dislocation or dysplasia of the hip and pectus excavatum. Approximately 80% of these patients will have some degree of vesicoureteral reflux, which can predispose to urinary tract infection. Despite the marked dilatation of the urinary tract, most children with prune-belly syndrome have adequate renal parenchyma for growth and development.