Hemifacial microsomia (craniofacial microsomia):
Is relatively common with an incidence of 1:3000-1:5000. The mandibular hypoplasia was classified by Pruzansky (Muerman described ear deformity). OMENS is another classification which describes ocular, mandibular, ear, nerve and soft tissue deficiencies. Osseodistraction is first-line treatment for most skeletal correction. Orbital dystopia is common.
Treacher-Collins syndrome consists of all except:
Micrognathia.
With regard to giant congenital naevi:
They are defined as greater than 5% body surface area. Giant congenital naevi are defined as >5% surface area or 20cm in diameter. Because the naevi are more superficial and mature (travel deeper) with time, early treatment with ablative modalities may be more efficacious. The malignant potential is controversial with widely quoted rates from 2-40% (approximate) but significant evidence points towards a lesser risk than previously thought and 50% would be an exaggerated risk.
Neonatal splintage can be used to correct:
Prominent ears and Stahl’s bar.
Extravasation injuries with non-isotonic agents are not infrequent in infants. Which is not true regarding management of these injuries?
Always remove the cannula. This is incorrect; the cannula may be of benefit in treatment if it is kept in situ to help with lavage or administration of an antidote. The infusion pump should be stopped immediately if that is the source. Injection of hyaluronidase and flushes with saline through multiple stab incisions around the area can help reduce the extent of tissue damage. Excision and grafting or other methods of reconstruction may be required, but usually as a delayed procedure.